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BCKDHB Rabbit anti-Human, Polyclonal, Invitrogen™

Rabbit Polyclonal Antibody

Manufacturer:  Invitrogen PA524166

Catalog No. PIPA524166


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Description

Description

Branched-chain keto acid dehydrogenase is a multienzyme complex associated with the inner membrane of mitochondria, and functions in the catabolism of branched-chain amino acids. The complex consists of multiple copies of 3 components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). This gene encodes the E1 beta subunit, and mutations therein have been associated with maple syrup urine disease (MSUD), type 1B, a disease characterized by a maple syrup odor to the urine in addition to mental and physical retardation, and feeding problems.
Specifications

Specifications

BCKDHB
Polyclonal
PBS with 0.09% sodium azide
P21953
E1B, dJ279A18.1, 2-oxoisovalerate dehydrogenase beta subunit, 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial, BCKDE1B, BCKDH E1-beta, E1b-beta subunit of the branched-chain complex, branched chain alpha-ketoacid dehydrogenase E1-beta subunit, branched-chain alpha-ke
Rabbit
IgG
400 μL
-20° C, Avoid Freeze/Thaw Cycles
Primary
594
Flow Cytometry, Immunocytochemistry, Immunofluorescence, Immunohistochemistry, Western Blot
Unconjugated
BCKDHB
Liquid
BCKDHB
KLH conjugated synthetic peptide between 41-70 amino acids from the N-terminal region of human BCKDHB
Antigen affinity chromatography
RUO
Antibody
Polyclonal
Human
Documents
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