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TRPML1 Rabbit anti-Human, Mouse, Rat, Polyclonal, Invitrogen™

Rabbit Polyclonal Antibody

Manufacturer:  Invitrogen PA146474

Catalog No. PA146474


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Description

Description

The target sequence has 85% sequence homology with monkey and 78% sequence homology with bovine. Suggested positive control: mouse brain protein.

Defects in Mucolipin-1 are the cause of mucolipidosis type IV (MLIV), also known as sialolipidosis. MLIV is an autosomal recessive lysosomal storage disorder characterized by severe psychomotor retardation and ophthalmologic abnormalities, including corneal opacity, retinal degeneration and strabismus. Storage bodies of lipids and water-soluble substances are seen by electron microscopy in almost every cell type of the patients. Most patients are unable to speak or walk independently and reach a maximal developmental level of 1-2 years. All patients have constitutive achlorhydia associated with a secondary elevation of serum gastrin levels.
Specifications

Specifications

TRPML1
Polyclonal
Unconjugated
MCOLN1
Liquid
MCOLN1
Synthetic peptide corresponding to residues 500-580 of a C-terminal portion of mouse Mucolipin-1. [Swiss-ProtNo. Q99J21]
Antigen affinity chromatography
RUO
Antibody
Polyclonal
Human, Mouse, Rat
Western Blot
1.0 mg/mL
PBS with 0.02% sodium azide
Q9GZU1, Q99J21
Mucolipidin , MG-2 , MCOLN1 , ML4 , MSTP080 , TRPML1 , TRPML-1 anti
Rabbit
IgG
100 μL
Store at 4°C short term. For long term storage, store at -20°C, avoiding freeze/thaw cycles.
Primary
288371, 57192, 94178
Documents
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