HPS1 Rabbit anti-Human, Polyclonal, Proteintech
Rabbit Polyclonal Antibody
Manufacturer: Proteintech Group Inc 150771AP
DescriptionHermansky-Pudlak syndrome (HPS) is a rare, genetically heterogeneous, autosomal recessive disorder. It is characterized by oculocutaneous albinism, lysosomal storage defects and prolonged bleeding due to platelet storage pool deficiency. There are 10 HPS genes encoding HPS proteins that all interact within three distinct ubiquitously expressed protein complexes or biogenesis of lysosome-related organelle complexes. Defects in these genes cause HPS. HSP-1 is a component of multiple cytoplasmic organelles and is important for their normal development and function. It plays a role in intracellular protein sorting.
|PBS with 50% glycerol and 0.02% sodium azide; pH 7.3|
|Hermansky Pudlak syndrome 1, HPS, HPS1|
|Immunocytochemistry, Immunofluorescence, Western Blot|
|HPS1 Fusion Protein Ag7149|
|Antigen Affinity Chromatography|
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