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NAGA Mouse anti-Human, Clone: OTI3A4, Invitrogen™

Mouse Monoclonal Antibody

Manufacturer:  Invitrogen MA527447

Catalog No. PIMA527447


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Description

Description

NAGA (N-acetylgalactosaminidase, alpha), also known as alpha-galactosidase B or GALB, is a 411 lysosomal protein belonging to the glycosyl hydrolase 27 family that may exist as a homodimer and plays a critical role in glycolipid breakdown. NAGA encodes alpha-N-acetylgalactosaminidase, a lysosomal enzyme, which cleaves alpha-N-acetylgalactosaminyl groups from glycoconjugates. Mapping to human chromosome 22q13.2, NAGA defects are the cause of an autosomal recessive disorder with three phenotypes, known as Schindler disease (types I, II and III) or NAGA deficiency (types I, II and III). Characterized by neurologic manifestations that range in severity, Schindler disease type I is the most severe form, followed by type III, which may have mild-to-moderate effects. Schindler disease type II, also known as Kanzaki disease, is characterized by mild intellectual impairment and angiokeratoma corporis diffusum.
Specifications

Specifications

NAGA
Monoclonal
1 mg/mL
PBS with 1% BSA, 50% glycerol and 0.02% sodium azide; pH 7.3
P17050
NAGA, alpha-N- (alpha-galactosidase B), alpha-N-acetylgalactosaminidase, EC 3.2.1, EC 3.2.1.49, GALB, N-acetylgalactosaminidase, alpha-
Mouse
IgG1
100 μL
-20° C, Avoid Freeze/Thaw Cycles
Primary
4668
Immunohistochemistry (Paraffin), Western Blot
OTI3A4
Unconjugated
NAGA
Liquid
NAGA
Full length human recombit protein of NAGA produced in HEK293T cell
Affinity Chromatography
RUO
Antibody
Monoclonal
Human
Documents
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