PCCA Rabbit anti-Human, Mouse, Polyclonal, Proteintech
Rabbit Polyclonal Antibody
Manufacturer: Proteintech Group Inc 219881AP
This antibody is specific to PCCA.This protein is a key enzyme in the catabolic pathway of odd-chain fatty acids, isoleucine, threonine, methionine, and valine. It is probably a dodecamer composed of six biotin-containing alpha subunits and six beta subunits. The protein is located in the mitochondrial matrix. Defects in PCCA are the cause o fpropionic acidemia type I (PA-1) [MIM:606054]. PA-1 is a life-threatening disease characterized by episodic vomiting, lethargy and ketosis, neutropenia, periodic thrombocytopenia, hypogammaglobulinemia, develop-mental retardation, and intolerance to protein.
|PBS with 50% glycerol and 0.02% sodium azide; pH 7.3|
|PCCA, PCCase subunit alpha|
|Immunohistochemistry (Paraffin), Immunoprecipitation, Western Blot|
|PCCA Fusion Protein Ag17271|
|Antigen Affinity Chromatography|
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