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PCCA Mouse anti-Human, Clone: OTI1E9, Invitrogen™

Mouse Monoclonal Antibody

Manufacturer:  Invitrogen MA527386

Catalog No. PIMA527386


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Description

Description

This protein is a key enzyme in the catabolic pathway of odd-chain fatty acids, isoleucine, threonine, methionine, and valine. It is probably a dodecamer composed of six biotin-containing alpha subunits and six beta subunits. The protein is located in the mitochondrial matrix. Defects in PCCA are the cause o fpropionic acidemia type I (PA-1) PA-1 is a life-threatening disease characterized by episodic vomiting, lethargy and ketosis, neutropenia, periodic thrombocytopenia, hypogammaglobulinemia, develop-mental retardation, and intolerance to protein.
Specifications

Specifications

PCCA
Monoclonal
1 mg/mL
PBS with 1% BSA, 50% glycerol and 0.02% sodium azide; pH 7.3
P05165
PCCase alpha subunit, pccA complementation group, propanoyl-CoA:carbon dioxide ligase alpha subunit, propionyl Coenzyme A carboxylase, alpha polypeptide, propionyl-CoA carboxylase alpha chain, mitochondrial
Mouse
IgG1
100 μL
-20° C, Avoid Freeze/Thaw Cycles
Primary
5095
Immunohistochemistry (Paraffin), Western Blot
OTI1E9
Unconjugated
PCCA
Liquid
PCCA
Full length human recombit protein of PCCA produced in HEK293T cell
Affinity Chromatography
RUO
Antibody
Monoclonal
Human
Documents
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