ALAS2 Mouse anti-Human, Clone: OTI2D3, liquid, TrueMAB™

Mouse Monoclonal Antibody

Supplier:  OriGene TA809959

Catalog No. 50-168-3120

Description

ALAS2 specifies an erythroid-specific mitochondrially located enzyme. It catalyzes the first step in the heme biosynthetic pathway. Defects in this gene cause X-linked pyridoxine-responsive sideroblastic anemia.The product of this gene specifies an erythroid-specific mitochondrially located enzyme. The encoded protein catalyzes the first step in the heme biosynthetic pathway. Defects in this gene cause X-linked pyridoxine-responsive sideroblastic anemia. Alternatively spliced transcript variants encoding different isoforms have been identified.

Specifications

• Antigen: ALAS2
• Classification: Monoclonal
• Concentration: 1 mg/mL
• Formulation: PBS with 1% BSA, 50% glycerol and 0.02% sodium azide
• Gene Accession No.: P22557
• Gene Symbols: ALAS2
• Immunogen: Human recombit protein fragment corresponding to amino acids 139-287 of human ALAS2 produced in E.coli.
• Quantity: 100 μL
• Primary or Secondary: Primary
• Target Species: Human
• Product Type: Antibody
• Isotype: IgG1

• Applications: Western Blot
• Clone: OTI2D3
• Conjugate: Unconjugated
• Gene: ALAS2
• Gene Alias: ALAS-E, ALASE, ANH1, ASB, SIDBA1, XLDPP, XLEPP, XLSA
• Host Species: Mouse
• Purification Method: Affinity Chromatography
• Regulatory Status: RUO
• Gene ID (Entrez): 212
• Content And Storage: -20° C, Avoid Freeze/Thaw Cycles
• Form: Liquid