anti-PEX19 Matched Antibody Pair, Abnova

Supplier:  Abnova Corporation H00005824AP11

Catalog No. 89-017-335

Includes: Rabbit MaxPab™ affinity purified polyclonal anti-PEX19 (100μg); Mouse monoclonal anti-PEX19, IgG2aκ (20μg); Sufficient for at least 3-5 x 96 well plates using recommended protocols.

Description

This gene is necessary for early peroxisomal biogenesis. It acts both as a cytosolic chaperone and as an import receptor for peroxisomal membrane proteins (PMPs). Peroxins (PEXs) are proteins that are essential for the assembly of functional peroxisomes. The peroxisome biogenesis disorders (PBDs) are a group of genetically heterogeneous autosomal recessive, lethal diseases characterized by multiple defects in peroxisome function. The peroxisomal biogenesis disorders are a heterogeneous group with at least 14 complementation groups and with more than 1 phenotype being observed in cases falling into particular complementation groups. Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in this gene are a cause Zellweger syndrome (ZWS).

ELISA

Specifications

• Antigen: PEX19
• Classification: Monoclonal/Polyclonal
• Description: This antibody pair set comes with matched antibody pair to detect and quantify protein level of human PEX19.
• Gene Alias: D1S2223E/HK33/PMP1/PMPI/PXF/PXMP1
• Host Species: Mouse, Rabbit
• Quantity: 1 Set
• Primary or Secondary: Primary
• Includes: Antibody pair set content: 1. Capture antibody: rabbit MaxPab™ affinity purified polyclonal anti-PEX19 (100 μg) 2. Detection antibody: mouse monoclonal anti-PEX19, IgG2a Kappa (20 μg) *Reagents are sufficient for at least 1-2 x 96 well plates using recommended protocols.
• Content And Storage: Store reagents of the antibody pair set at -20°C or lower. Please aliquot to avoid repeated freeze thaw cycle. Reagents should be returned to -20°C storage immediately after use.

• Applications: ELISA
• Conjugate: Unconjugated
• Gene: PEX19
• Gene Symbols: PEX19
• Purification Method: Affinity Purified
• Regulatory Status: RUO
• Gene ID (Entrez): 5824
• Target Species: Human
• Isotype: IgG2a