BCS1L Mouse anti-Human, Mouse, Clone: 3G6H1, Proteintech

Mouse Monoclonal Antibody

Supplier:  Proteintech Group Inc 602121IG150UL

Catalog No. 50-173-6315

Description

This gene encodes a homolog of the S. cerevisiae bcs1 protein which is involved in the assembly of complex III of the mitochondrial respiratory chain. The encoded protein does not contain a mitochondrial targeting sequence but experimental studies confirm that it is imported into mitochondria. Mutations in this gene are associated with mitochondrial complex III deficiency and the GRACILE syndrome. Five alternatively spliced transcripts encoding the same protein have been described.

Specifications

• Antigen: BCS1L
• Classification: Monoclonal
• Concentration: 0.86 mg/mL
• Formulation: PBS with 50% glycerol and 0.02% sodium azide; pH 7.3
• Gene Accession No.: Q9CZP5, Q9Y276
• Gene Symbols: BCS1L
• Immunogen: BCS1L Fusion Protein Ag18280
• Quantity: 150 μL
• Primary or Secondary: Primary
• Target Species: Human, Mouse
• Product Type: Antibody
• Isotype: IgG1

• Applications: Immunocytochemistry, Immunofluorescence, Immunohistochemistry (Paraffin), Western Blot
• Clone: 3G6H1
• Conjugate: Unconjugated
• Gene: BCS1L
• Gene Alias: BCS1L, BJS, FLNMS, GRACILE, h BCS, h BCS1, Hs.6719, Mitochondrial chaperone BCS1, PTD
• Host Species: Mouse
• Purification Method: Protein G
• Regulatory Status: RUO
• Gene ID (Entrez): 617, 66821
• Content And Storage: -20°C
• Form: Liquid