PCCA Rabbit anti-Human, Mouse, Polyclonal, Proteintech

Rabbit Polyclonal Antibody

Catalog Number	Mfr. No.	Quantity
50-173-3670	Proteintech Group Inc 219881AP150UL	150 μL

Description

This antibody is specific to PCCA.

This protein is a key enzyme in the catabolic pathway of odd-chain fatty acids, isoleucine, threonine, methionine, and valine. It is probably a dodecamer composed of six biotin-containing alpha subunits and six beta subunits. The protein is located in the mitochondrial matrix. Defects in PCCA are the cause o fpropionic acidemia type I (PA-1) [MIM:606054]. PA-1 is a life-threatening disease characterized by episodic vomiting, lethargy and ketosis, neutropenia, periodic thrombocytopenia, hypogammaglobulinemia, develop-mental retardation, and intolerance to protein.

Specifications

• Antigen: PCCA
• Applications: Immunohistochemistry (Paraffin), Immunoprecipitation, Western Blot
• Conjugate: Unconjugated
• Host Species: Rabbit
• Target Species: Human, Mouse
• Gene Accession No.: P05165, Q91ZA3
• Gene ID (Entrez): 110821, 5095
• Immunogen: PCCA Fusion Protein Ag17271
• Primary or Secondary: Primary
• Content And Storage: -20°C
• Gene: PCCA

• Concentration: 0.26 mg/mL
• Classification: Polyclonal
• Form: Liquid
• Regulatory Status: RUO
• Formulation: PBS with 50% glycerol and 0.02% sodium azide; pH 7.3
• Gene Alias: PCCA, PCCase subunit alpha
• Gene Symbols: PCCA
• Isotype: IgG
• Purification Method: Antigen Affinity Chromatography
• Product Type: Antibody