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isovaleryl Coenzyme A dehydrogenase, Mouse, Purified MaxPab™ Polyclonal Antibody, Abnova™
Mouse polyclonal antibody raised against a full-length human IVD protein.
Supplier: Abnova Corporation H00003712B01P
Description
Isovaleryl-CoA dehydrogenase (IVD) is a mitochondrial matrix enzyme that catalyzes the third step in leucine catabolism. The genetic deficiency of IVD results in an accumulation of isovaleric acid, which is toxic to the central nervous system and leads to isovaleric acidemia. Alternatively spliced transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq
Sequence: MATATRLLGWRVASWRLRPPLAGFVSQRAHSLLPVDDAINGLSEEQRQLRQTMAKFLQEHLAPKAQEIDRSNEFKNLREFWKQLGNLGVLGITAPVQYGGSGLGYLEHVLVMEEISRASGAVGLSYGAHSNLCINQLVRNGNEAQKEKYLPKLISGEYIGALAMSEPNAGSDVVSMKLKAEKKGNHYILNGNKFWITNGPDADVLIVYAKTDLAAVPASRGITAFIVEKGMPGFSTSKKLDKLGMRGSNTCELIFEDCKIPAANILGHENKGVYVLMSGLDLERLVLAGGPLGLMQAVLDHTIPYLHVREAFGQKIGHFQLMQGKMADMYTRLMACRQYVYNVAKACDEGHCTAKDCAGVILYSAECATQVALDGIQCFGGNGYINDFPMGRFLRDAKLYEIGAGTSEVRRLVIGRAFNADFHSpecifications
isovaleryl Coenzyme A dehydrogenase | |
Polyclonal | |
Mouse polyclonal antibody raised against a full-length human IVD protein. | |
IVD | |
ACAD2 | |
Mouse | |
Affinity Purified | |
RUO | |
Primary | |
Human | |
Antibody |
Western Blot | |
Unconjugated | |
PBS with no preservative; pH 7.4 | |
NM_002225.2 | |
IVD | |
IVD (NP_002216.1, 1 a.a. ∼ 423 a.a) full-length human protein. | |
50 μg | |
Stem Cell Biology | |
3712 | |
Store at -20°C or lower. Aliquot to avoid repeated freezing and thawing. | |
IgG |
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