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peroxisomal biogenesis factor 7, Mouse, Polyclonal Antibody, Abnova™

Mouse polyclonal antibody raised against a partial recombinant PEX7.

Supplier:  Abnova Corporation H00005191A01

Catalog No. 89-004-234


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Description

Description

This gene encodes the cytosolic receptor for the set of peroxisomal matrix enzymes targeted to the organelle by the peroxisome targeting signal 2 (PTS2). Defects in this gene cause peroxisome biogenesis disorders (PBDs), which are characterized by multiple defects in peroxisome function. There are at least 14 complementation groups for PBDs, with more than one phenotype being observed in cases falling into particular complementation groups. Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in this gene have been associated with PBD complementation group 11 (PBD-CG11) disorders, rhizomelic chondrodysplasia punctata type 1 (RCDP1), and Refsum disease (RD). [provided by RefSeq

Sequence: SAVCGGAARMLRTPGRHGYAAEFSPYLPGRLACATAQHYGIAGCGTLLILDPDEAGLRLFRSFDWNDGLFDVTWSENNEHVLITCSGDGSLQLWDTAK
Specifications

Specifications

peroxisomal biogenesis factor 7
Polyclonal
Mouse polyclonal antibody raised against a partial recombinant PEX7.
PEX7
PTS2R/RCDP1/RD
Mouse
50 μL
Membrane Receptors
Primary
Human, Mouse
Serum
ELISA, Western Blot
Unconjugated
50% glycerol
NM_000288
PEX7
PEX7 (NP_000279, 2 a.a. ∼ 99 a.a) partial recombinant protein with GST tag.
RUO
Yes
5191
Store at -20°C or lower. Aliquot to avoid repeated freezing and thawing.
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