Invitrogen™ CIRH1A Polyclonal Antibody

Rabbit Polyclonal Antibody

Supplier:  Invitrogen™ PA559445

Catalog No. PIPA559445

Description

Immunogen sequence: FPVTAMAIAP NTNNLVIAHS DQQVFEYSIP DKQYTDWSRT VQKQGFHHLW LQRDTPITHI SFHPKRPMHI LLHDAYMFCI IDKSLPLPND KTLLYNPFPL T Highest antigen sequence identity to the following orthologs: Mouse - 88%, Rat - 90%.

CIRH1A encodes a WD40-repeat-containing protein that is localized to the nucleolus. Mutation of this gene causes North American Indian childhood cirrhosis, a severe intrahepatic cholestasis that results in transient neonatal jaundice, and progresses to periportal fibrosis and cirrhosis in childhood and adolescence.

Specifications

• Antigen: CIRH1A
• Classification: Polyclonal
• Conjugate: Unconjugated
• Gene: UTP4
• Gene Alias: CIRH1A; Cirhin; cirrhosis, autosomal recessive 1A (cirhin); cirrhosis, autosomal recessive 1A (human); cPERP-E; Kiaa1988; Naic; Teg-292; testis expressed gene 292; testis-expressed gene 292; testis-expressed gene 292 protein; Tex292; U3 small nucleolar RNA-associated protein 4 homolog; UTP4; UTP4 small subunit (SSU) processome component; UTP4 small subunit processome component; UTP4, small subunit (SSU) processome component, homolog; UTP4, small subunit processome component
• Host Species: Rabbit
• Purification Method: Antigen affinity chromatography
• Regulatory Status: RUO
• Gene ID (Entrez): 84916
• Content And Storage: Store at 4°C short term. For long term storage, store at -20°C, avoiding freeze/thaw cycles.
• Form: Liquid

• Applications: Immunohistochemistry (Paraffin), Western Blot
• Concentration: 0.1 mg/mL
• Formulation: PBS with 40% glycerol and 0.02% sodium azide; pH 7.2
• Gene Accession No.: Q969X6
• Gene Symbols: UTP4
• Immunogen: Recombinant protein corresponding to Human CIRH1A. Recombinant protein control fragment (Product #RP-98567).
• Quantity: 100 μL
• Primary or Secondary: Primary
• Target Species: Human
• Product Type: Antibody
• Isotype: IgG