CPS1 Rabbit anti-Human, Mouse, Rat, Polyclonal, Proteintech
Rabbit Polyclonal Antibody
Manufacturer: Proteintech Group Inc 187031AP
The antibody can recognize two isoforms of this gene around 165 kDa and 116 kDa.The mitochondrial enzyme encoded by this gene catalyzes synthesis of carbamoyl phosphate from ammonia and bicarbonate. This reaction is the first committed step of the urea cycle, which is important in the removal of excess urea from cells. The encoded protein may also represent a core mitochondrial nucleoid protein. Three transcript variants encoding different isoforms have been found for this gene. The shortest isoform may not be localized to the mitochondrion. Mutations in this gene have been associated with carbamoyl phosphate synthetase deficiency, susceptibility to persistent pulmonary hypertension, and susceptibility to venoocclusive disease after bone marrow transplantation.
|PBS with 50% glycerol and 0.02% sodium azide; pH 7.3|
|P07756, P31327, Q8C196|
|CPS1, CPSase I|
|1373, 227231, 497840|
|Immunocytochemistry, Immunofluorescence, Western Blot|
|Antigen Affinity Chromatography|
|Human, Mouse, Rat|
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