DBT Monoclonal Antibody (OTI1G2), TrueMAB™, OriGene

Mouse Monoclonal Antibody

Supplier:  OriGene TA504748

Catalog No. 50-167-5368

Description

The branched-chain alpha-keto acid dehydrogenase complex (BCKD) is an inner-mitochondrial enzyme complex involved in the breakdown of the branched-chain amino acids isoleucine, leucine, and valine. The BCKD complex is thought to be composed of a core of 24 transacylase (E2) subunits, and associated decarboxylase (E1), dehydrogenase (E3), and regulatory subunits. This gene encodes the transacylase (E2) subunit. Mutations in this gene result in maple syrup urine disease, type 2. Alternatively spliced transcript variants have been described, but their biological validity has not been determined.

Specifications

• Antigen: DBT
• Classification: Monoclonal
• Concentration: 1 mg/mL
• Formulation: PBS with 1% BSA, 50% glycerol and 0.02% sodium azide
• Gene Accession No.: P11182
• Gene Symbols: DBT
• Immunogen: Full length human recombit protein of human DBT produced in HEK293T cell.
• Quantity: 100 μL
• Primary or Secondary: Primary
• Target Species: Human
• Product Type: Antibody
• Isotype: IgG1

• Applications: Flow Cytometry, Western Blot
• Clone: OTI1G2
• Conjugate: Unconjugated
• Gene: DBT
• Gene Alias: BCATE2, BCKAD-E2, BCKADE2, BCOADC-E2, E2, E2B
• Host Species: Mouse
• Purification Method: Affinity Chromatography
• Regulatory Status: RUO
• Gene ID (Entrez): 1629
• Content And Storage: -20° C, Avoid Freeze/Thaw Cycles
• Form: Liquid