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Invitrogen™ Dysferlin Recombinant Rabbit Monoclonal Antibody (JF05-54)
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Catalog No. PIMA532524
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100 μL
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PIMA532524 100 μL
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Catalog No. PIMA532524 Supplier Invitrogen™ Supplier No. MA532524
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Description

Rabbit Recombinant Monoclonal Antibody

Recombinant rabbit monoclonal antibodies are produced using in vitro expression systems. The expression systems are developed by cloning in the specific antibody DNA sequences from immunoreactive rabbits. Then, individual clones are screened to select the best candidates for production. The advantages of using recombinant rabbit monoclonal antibodies include: better specificity and sensitivity, lot-to-lot consistency, animal origin-free formulations, and broader immunoreactivity to diverse targets due to larger rabbit immune repertoire.

Dysferlin is the protein product of the 2p13 gene that is defective in patients with Limb-Girdle Muscular Dystrophy type 2B (LGMD2B) and Miyoshi Myopathy (MM). Dysferlin is normally localized to the muscle plasma membrane. In patients with LGMD2B and MM, immunoreactivity to dysferlin is severely reduced or lost, depending on the type of mutation. This antibody is used for the characterization of LGMD2B and MM.
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Specifications

Antigen Dysferlin
Applications Immunohistochemistry (Paraffin), Western Blot, Immunocytochemistry, Western Blot
Classification Recombinant Monoclonal
Clone JF05-54
Concentration 1 mg/mL
Conjugate Unconjugated
Formulation TBS with 0.05% BSA, 40% Glycerol and 0.05% sodium azide; pH 7.4
Gene DYSF
Gene Accession No. O75923, Q9ESD7
Gene Alias 2310004N10Rik; AI604795; D6Pas3; Dysf; Dysferlin; dysferlin variant a; dysferlin_a; dystrophy-associated fer-1-like 1; dystrophy-associated fer-1-like protein; FER1L1; fer-1-like family member 1; fer-1-like protein 1; FLJ00175; FLJ90168; LGMD2B; limb girdle muscular dystrophy 2B (autosomal recessive); MMD1
Gene Symbols DYSF
Host Species Rabbit
Immunogen Synthetic peptide within Human Dysferlin aa 113-162.
Purification Method Protein A
Quantity 100 μL
Regulatory Status RUO
Primary or Secondary Primary
Gene ID (Entrez) 26903, 8291
Target Species Human, Mouse
Content And Storage Store at 4°C short term. For long term storage, store at -20°C, avoiding freeze/thaw cycles.
Product Type Antibody
Form Liquid
Isotype IgG
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