Invitrogen™ FKRP Polyclonal Antibody

Rabbit Polyclonal Antibody

Supplier:  Invitrogen™ PA565349

Catalog No. PIPA565349

Description

Immunogen sequence: ETARYVVGVLE AAGVRYWLEG GSLLGAARHG DIIPWDYDVD LGIYLEDVGN CEQLRGAEAG SVVDERGFVW EKAVEGDF Highest antigen sequence identity to the following orthologs - mouse 100%, rat 100%.

This gene encodes a protein which is targeted to the medial Golgi apparatus and is necessary for posttranslational modification of dystroglycan. Mutations in this gene have been associated with congenital muscular dystrophy, mental retardation, and cerebellar cysts. Several alternatively spliced transcript variants of this gene have been described, but the full-length nature of some of these variants has not been determined. [provided by RefSeq, Oct 2008].

Specifications

• Antigen: FKRP
• Classification: Polyclonal
• Conjugate: Unconjugated
• Gene: FKRP
• Gene Alias: A830029B19Rik; AI842067; AI847300; FKRP; fukutin related protein; fukutin-related protein; LGMD1I; LGMD2I; MDC1C; MDDGA5; MDDGB5; MDDGC5; Ribitol-5-phosphate transferase
• Host Species: Rabbit
• Purification Method: Antigen affinity chromatography
• Regulatory Status: RUO
• Gene ID (Entrez): 79147
• Content And Storage: Store at 4°C short term. For long term storage, store at -20°C, avoiding freeze/thaw cycles.
• Form: Liquid

• Applications: Immunocytochemistry
• Concentration: 0.10 mg/mL
• Formulation: PBS with 40% glycerol and 0.02% sodium azide; pH 7.2
• Gene Accession No.: Q9H9S5
• Gene Symbols: FKRP
• Immunogen: Recombinant Human FKRP. Recombinant protein control fragment (Product #RP-99940).
• Quantity: 100 μL
• Primary or Secondary: Primary
• Target Species: Human
• Product Type: Antibody
• Isotype: IgG