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Invitrogen™ GAA Polyclonal Antibody
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Catalog No. PIPA596756
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100 μL
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PIPA596756 100 μL
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Catalog No. PIPA596756 Supplier Invitrogen™ Supplier No. PA596756
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Description

Rabbit Polyclonal Antibody

Positive Samples: LO2, HT-29, 293T, A-549, DU145, Mouse liver, Mouse heart, Mouse thymus, Rat liver; Cellular Location: Lysosome, Lysosome membrane.

This gene encodes acid alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. Different forms of acid alpha-glucosidase are obtained by proteolytic processing. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum. Three transcript variants encoding the same protein have been found for this gene.
TRUSTED_SUSTAINABILITY

Specifications

Antigen GAA
Applications ELISA, Western Blot, Immunocytochemistry
Classification Polyclonal
Concentration 2.49 mg/mL
Conjugate Unconjugated
Formulation PBS with 50% glycerol and 0.02% sodium azide; pH 7.3
Gene Gaa
Gene Accession No. P10253, P70699, Q6P7A9
Gene Alias 70 kDa lysosomal alpha-glucosidase; 76 kDa lysosomal alpha-glucosidase; acid (Pompe disease, glycogen storage disease type II); acid alpha-glucosidase; acid maltase; Aglucosidase alfa; E430018M07Rik; Gaa; glucosidase alpha, acid; glucosidase, alpha, acid; glucosidase, alpha; acid (Pompe disease, glycogen storage disease type II); LYAG; Lysosomal alpha-glucosidase
Gene Symbols Gaa
Host Species Rabbit
Immunogen Recombinant protein (or fragment).
Purification Method Affinity Chromatography
Quantity 100 μL
Regulatory Status RUO
Primary or Secondary Primary
Gene ID (Entrez) 14387, 2548, 367562
Target Species Human, Mouse, Rat
Content And Storage -20°C, Avoid Freeze/Thaw Cycles
Product Type Antibody
Form Liquid
Isotype IgG
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