Invitrogen™ GAA Recombinant Rabbit Monoclonal Antibody (5L2L10)

Catalog No.	Quantity
PIMA537870	100 μL

Catalog No. PIMA537870

Supplier: Invitrogen™ MA537870

Description

Rabbit Recombinant Monoclonal Antibody

Positive Samples: 293T, HepG2, DU145.

This gene encodes acid alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. Different forms of acid alpha-glucosidase are obtained by proteolytic processing. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum. Three transcript variants encoding the same protein have been found for this gene.

Specifications

• Antigen: GAA
• Applications: ELISA, Western Blot
• Classification: Recombinant Monoclonal
• Clone: 5L2L10
• Concentration: 0.8 mg/mL
• Conjugate: Unconjugated
• Formulation: PBS with 0.05% BSA, 50% glycerol and 0.02% sodium azide; pH 7.3
• Gene: Gaa
• Gene Accession No.: P10253
• Gene Alias: 70 kDa lysosomal alpha-glucosidase; 76 kDa lysosomal alpha-glucosidase; acid (Pompe disease, glycogen storage disease type II); acid alpha-glucosidase; acid maltase; Aglucosidase alfa; E430018M07Rik; Gaa; glucosidase alpha, acid; glucosidase, alpha, acid; glucosidase, alpha; acid (Pompe disease, glycogen storage disease type II); LYAG; Lysosomal alpha-glucosidase
• Gene Symbols: Gaa
• Host Species: Rabbit
• Immunogen: Synthetic peptide.
• Purification Method: Affinity chromatography
• Quantity: 100 μL
• Regulatory Status: RUO
• Primary or Secondary: Primary
• Gene ID (Entrez): 2548
• Target Species: Human
• Content And Storage: -20°C, Avoid Freeze/Thaw Cycles
• Product Type: Antibody
• Form: Liquid
• Isotype: IgG

Safety and Handling

WARNING: Cancer - www.P65Warnings.ca.gov