Invitrogen™ GNS Polyclonal Antibody

Rabbit Polyclonal Antibody

Supplier:  Invitrogen™ PA569372

Catalog No. PIPA569372

Description

This target displays homology in the following species: Cow: 100%; Dog: 100%; Goat: 100%; Guinea Pig: 100%; Horse: 100%; Human: 100%; Mouse: 100%; Rabbit: 100%; Rat: 100%; Zebrafish: 92%.

GNS is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparan sulphate, and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder mucopolysaccharidosis type IIID (Sanfilippo D syndrome). Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome.

Specifications

• Antigen: GNS
• Classification: Polyclonal
• Conjugate: Unconjugated
• Gene: GNS
• Gene Alias: 2610016K11Rik; AU042285; C87209; G6S; glucosamine (N-acetyl)-6-sulfatase; glucosamine (N-acetyl)-6-sulfatase (Sanfilippo disease IIID); glucosamine -6-sulfatase; glucosamine-6-sulfatase; Gns; N28088; N-acetylglucosamine 6-sulfatase precursor; N-acetylglucosamine-6-sulfatase
• Host Species: Rabbit
• Purification Method: Affinity chromatography
• Regulatory Status: RUO
• Gene ID (Entrez): 299825
• Content And Storage: -20°C, Avoid Freeze/Thaw Cycles
• Form: Liquid

• Applications: Western Blot
• Concentration: 0.5 mg/mL
• Formulation: PBS with 2% sucrose and 0.09% sodium azide
• Gene Accession No.: 0
• Gene Symbols: GNS
• Immunogen: synthetic peptide corresponding to a region of rat GNS.
• Quantity: 100 μL
• Primary or Secondary: Primary
• Target Species: Rat
• Product Type: Antibody
• Isotype: IgG