Invitrogen™ GNS Polyclonal Antibody

Rabbit Polyclonal Antibody

Supplier:  Invitrogen™ PA587320

Catalog No. PIPA587320

Description

Purity is > 95% by SDS-PAGE.

GNS is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparan sulphate, and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder mucopolysaccharidosis type IIID (Sanfilippo D syndrome). Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome.

Specifications

• Antigen: GNS
• Classification: Polyclonal
• Conjugate: Unconjugated
• Gene: GNS
• Gene Alias: 2610016K11Rik; AU042285; C87209; G6S; glucosamine (N-acetyl)-6-sulfatase; glucosamine (N-acetyl)-6-sulfatase (Sanfilippo disease IIID); glucosamine -6-sulfatase; glucosamine-6-sulfatase; Gns; N28088; N-acetylglucosamine 6-sulfatase precursor; N-acetylglucosamine-6-sulfatase
• Host Species: Rabbit
• Purification Method: Antigen affinity chromatography
• Regulatory Status: RUO
• Gene ID (Entrez): 2799, 299825, 75612
• Content And Storage: Store at 4°C short term. For long term storage, store at -20°C, avoiding freeze/thaw cycles.
• Form: Liquid

• Applications: Western Blot
• Concentration: 1 mg/mL
• Formulation: PBS with 50% glycerol and 0.02% sodium azide; pH 7.2
• Gene Accession No.: P15586, Q8BFR4
• Gene Symbols: GNS
• Immunogen: Recombinant full length Human GNS.
• Quantity: 100 μL
• Primary or Secondary: Primary
• Target Species: Human, Mouse, Rat
• Product Type: Antibody
• Isotype: IgG

Safety and Handling

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