HADHA Monoclonal Antibody (OTI7B3), TrueMAB™, OriGene

Catalog No.	Quantity
50-168-4424	100 μL

Catalog No. 50-168-4424 Supplier OriGene Supplier No. TA812134

Description

Mouse Monoclonal Antibody

This gene encodes the alpha subunit of the mitochondrial trifunctional protein, which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. The mitochondrial membrane-bound heterocomplex is composed of four alpha and four beta subunits, with the alpha subunit catalyzing the 3-hydroxyacyl-CoA dehydrogenase and enoyl-CoA hydratase activities. Mutations in this gene result in trifunctional protein deficiency or LCHAD deficiency. The genes of the alpha and beta subunits of the mitochondrial trifunctional protein are located adjacent to each other in the human genome in a head-to-head orientation.

Specifications

• Antigen: HADHA
• Applications: Western Blot
• Classification: Monoclonal
• Clone: OTI7B3
• Concentration: 1 mg/mL
• Conjugate: Unconjugated
• Formulation: PBS with 1% BSA, 50% glycerol and 0.02% sodium azide
• Gene: HADHA
• Gene Accession No.: P40939, Q64428
• Gene Alias: ECHA, GBP, HADH, LCEH, LCHAD, MTPA, TP-ALPHA
• Gene Symbols: Hadha
• Host Species: Mouse
• Immunogen: Human recombit protein fragment corresponding to amino acids 106-325 of human HADHA produced in E.coli.
• Purification Method: Affinity Chromatography
• Quantity: 100 μL
• Regulatory Status: RUO
• Primary or Secondary: Primary
• Gene ID (Entrez): 170670, 3030
• Target Species: Human, Rat
• Content And Storage: -20° C, Avoid Freeze/Thaw Cycles
• Product Type: Antibody
• Form: Liquid
• Isotype: IgG1