HMBS Mouse anti-Human, Clone: OTI3E2, lyophilized, TrueMAB
Mouse Monoclonal Antibody
Manufacturer: OriGene CF802728
Reconstitute with PBS (pH 7.3) and recommend to perform another round of desalting process using Product No. 7KMWCOPBGD (porphobilinogen deaminase), also designated hydroxymethylbilane synthase, is a cytoplasmic enzyme found in the heme synthesis pathway. PBGD belongs to the HMBS (hydroxymethylbilane synthase) family. Deficiency of PBGD causes errors in pyrrole metabolism, which in turn leads to an inherited autosomal disorder called acute intermittent porphyria (AIP). AIP is characterized by acute attacks of neurological dysfunctions with hypertension, tachycardia, peripheral neurologic disturbances, abdominal pain and excessive amounts of aminolevulinic acid and porphobilinogen in the urine.
|Full length human recombit protein of human HMBS produced in HEK293T cell.|
|PBS with 8% trehalose and no preservative; pH 7.3|
|PBG-D, PBGD, PORC, UPS|
|-20° C, Avoid Freeze/Thaw Cycles|
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