Learn More
HMBS Mouse anti-Human, Clone: OTI3E2, lyophilized, TrueMAB™

Mouse Monoclonal Antibody
Supplier: OriGene CF802728

Description
Reconstitute with PBS (pH 7.3) and recommend to perform another round of desalting process using Product No. 7KMWCO
PBGD (porphobilinogen deaminase), also designated hydroxymethylbilane synthase, is a cytoplasmic enzyme found in the heme synthesis pathway. PBGD belongs to the HMBS (hydroxymethylbilane synthase) family. Deficiency of PBGD causes errors in pyrrole metabolism, which in turn leads to an inherited autosomal disorder called acute intermittent porphyria (AIP). AIP is characterized by acute attacks of neurological dysfunctions with hypertension, tachycardia, peripheral neurologic disturbances, abdominal pain and excessive amounts of aminolevulinic acid and porphobilinogen in the urine.Specifications
HMBS | |
Monoclonal | |
Unconjugated | |
HMBS | |
PBG-D, PBGD, PORC, UPS | |
Mouse | |
Affinity Chromatography | |
RUO | |
3145 | |
-20° C, Avoid Freeze/Thaw Cycles | |
Lyophilized |
Western Blot | |
OTI3E2 | |
PBS with 8% trehalose and no preservative; pH 7.3 | |
P08397 | |
HMBS | |
Full length human recombit protein of human HMBS produced in HEK293T cell. | |
100 μg | |
Primary | |
Human | |
Antibody | |
IgG1 |
The Fisher Scientific Encompass Program offers items which are not part of our distribution portfolio. These products typically do not have pictures or detailed descriptions. However, we are committed to improving your shopping experience. Please use the form below to provide feedback related to the content on this product.