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HMBS Mouse anti-Human, Clone: OTI3E2, lyophilized, TrueMAB™ Non-distribution product as customer accommodation.

Mouse Monoclonal Antibody

Manufacturer:  OriGeneSupplier Diversity Partner CF802728

Catalog No. 50-166-6125


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Description

Description

Reconstitute with PBS (pH 7.3) and recommend to perform another round of desalting process using Product No. 7KMWCO

PBGD (porphobilinogen deaminase), also designated hydroxymethylbilane synthase, is a cytoplasmic enzyme found in the heme synthesis pathway. PBGD belongs to the HMBS (hydroxymethylbilane synthase) family. Deficiency of PBGD causes errors in pyrrole metabolism, which in turn leads to an inherited autosomal disorder called acute intermittent porphyria (AIP). AIP is characterized by acute attacks of neurological dysfunctions with hypertension, tachycardia, peripheral neurologic disturbances, abdominal pain and excessive amounts of aminolevulinic acid and porphobilinogen in the urine.
Specifications

Specifications

HMBS
Monoclonal
Unconjugated
HMBS
Lyophilized
HMBS
Full length human recombit protein of human HMBS produced in HEK293T cell.
Affinity Chromatography
RUO
Antibody
Monoclonal
Human
Western Blot
OTI3E2
PBS with 8% trehalose and no preservative; pH 7.3
P08397
PBG-D, PBGD, PORC, UPS
Mouse
IgG1
100 μg
-20° C, Avoid Freeze/Thaw Cycles
Primary
3145
SDS
Documents
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