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Invitrogen™ HPS1 Polyclonal Antibody

Rabbit Polyclonal Antibody

Supplier:  Invitrogen™ PA563938

Catalog No. PIPA563938


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Description

Description

Immunogen sequence: LWQGINLVLL TRSPSAPLAL VLSQLMDGFS MLEKKLKEGP EPGASLRSQP LVGDLRQRMD KFVKNRGAQE IQSTWLEFKA KAFSK Highest antigen sequence identity to the following orthologs: Mouse - 75%, Rat - 74%.

Hermansky-Pudlak syndrome (HPS) is a rare, genetically heterogeneous, autosomal recessive disorder. It is characterized by oculocutaneous albinism, lysosomal storage defects and prolonged bleeding due to platelet storage pool deficiency. There are 10 HPS genes encoding HPS proteins that all interact within three distinct ubiquitously expressed protein complexes or biogenesis of lysosome-related organelle complexes. Defects in these genes cause HPS. HSP-1 is a component of multiple cytoplasmic organelles and is important for their normal development and function. It plays a role in intracellular protein sorting.
TRUSTED_SUSTAINABILITY
Specifications

Specifications

HPS1
Polyclonal
Unconjugated
HPS1
6030422N11Rik; BB405864; BLOC3S1; ep; Gm21361; Hermansky-Pudlak syndrome 1 homolog (human); Hermansky-Pudlak syndrome 1 protein; Hermansky-Pudlak syndrome 1 protein homolog; Hermansky-Pudlak syndrome protein homolog; HPS; HPS1; HPS1, biogenesis of lysosomal organelles complex 3 subunit 1; MGC5277; pale ear
Rabbit
Antigen affinity chromatography
RUO
3257
Store at 4°C short term. For long term storage, store at -20°C, avoiding freeze/thaw cycles.
Liquid
Immunohistochemistry (Paraffin)
0.4 mg/mL
PBS with 40% glycerol and 0.02% sodium azide; pH 7.2
Q92902
HPS1
Recombinant protein corresponding to Human HPS1. Recombinant protein control fragment (Product #RP-101171).
100 μL
Primary
Human
Antibody
IgG
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