PAH/PH4H Rabbit anti-Human, Polyclonal, Bioss

Rabbit Polyclonal Antibody

Supplier:  Bioss BS21005R

Catalog No. 50-198-9923

Description

PAH encodes the enzyme phenylalanine hydroxylase that is the rate-limiting step in phenylalanine catabolism. Deficiency of this enzyme activity results in the autosomal recessive disorder phenylketonuria.

Specifications

• Antigen: PAH/PH4H
• Classification: Polyclonal
• Conjugate: Unconjugated
• Gene: PAH
• Gene Alias: AW106920; Pah; PH; Phe-4-monooxygenase; phenylalanine 4-monooxygenase; phenylalanine hydroxylase; Phenylalanine-4-hydroxylase; PKU; PKU1
• Host Species: Rabbit
• Purification Method: Protein A
• Regulatory Status: RUO
• Gene ID (Entrez): 5053
• Content And Storage: -20°C
• Form: Liquid

• Applications: Western Blot
• Concentration: 1 μg/mL
• Formulation: TBS with 1% BSA, 50% glycerol and 0.03% Proclin 300; pH
• Gene Accession No.: P00439
• Gene Symbols: PAH
• Immunogen: KLH conjugated synthetic peptide derived from human PAH/PH4H.
• Quantity: 100 μL
• Primary or Secondary: Primary
• Target Species: Human
• Product Type: Antibody
• Isotype: IgG