PEX7 Rabbit anti-Human, Mouse, Rat, Polyclonal, Proteintech

Rabbit Polyclonal Antibody

Catalog Number	Mfr. No.	Quantity
50-173-2988	Proteintech Group Inc 206141AP150UL	150 μL

Description

This gene encodes the cytosolic receptor for the set of peroxisomal matrix enzymes targeted to the organelle by the peroxisome targeting signal 2 (PTS2). Defects in this gene cause peroxisome biogenesis disorders (PBDs), which are characterized by multiple defects in peroxisome function. There are at least 14 complementation groups for PBDs, with more than one phenotype being observed in cases falling into particular complementation groups. Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in this gene have been associated with PBD complementation group 11 (PBD-CG11) disorders, rhizomelic chondrodysplasia punctata type 1 (RCDP1), and Refsum disease (RD).

Specifications

• Antigen: PEX7
• Applications: Western Blot
• Conjugate: Unconjugated
• Host Species: Rabbit
• Target Species: Human, Mouse, Rat
• Gene Accession No.: O00628, P97865
• Gene ID (Entrez): 18634, 308718, 5191
• Immunogen: PEX7 Fusion Protein Ag14666
• Primary or Secondary: Primary
• Content And Storage: -20°C
• Gene: PEX7

• Concentration: 0.45 mg/mL
• Classification: Polyclonal
• Form: Liquid
• Regulatory Status: RUO
• Formulation: PBS with 50% glycerol and 0.02% sodium azide; pH 7.3
• Gene Alias: Peroxin 7, PEX7, PTS2 receptor, PTS2R, RCDP1, RD
• Gene Symbols: Pex7
• Isotype: IgG
• Purification Method: Antigen Affinity Chromatography
• Product Type: Antibody