Invitrogen™ PPT1 Monoclonal Antibody (OTI1F10)

Mouse Monoclonal Antibody

Supplier:  Invitrogen™ MA526471

Catalog No. PIMA526471

Description

PPT1 Monoclonal Antibody for Western Blot, IHC (P)

The protein encoded by this gene is a small glycoprotein involved in the catabolism of lipid-modified proteins during lysosomal degradation. The encoded enzyme removes thioester-linked fatty acyl groups such as palmitate from cysteine residues. Defects in this gene are a cause of infantile neuronal ceroid lipofuscinosis 1 (CLN1, or INCL) and neuronal ceroid lipofuscinosis 4 (CLN4). Two transcript variants encoding different isoforms have been found for this gene.

Specifications

• Antigen: PPT1
• Classification: Monoclonal
• Concentration: 1 mg/mL
• Formulation: PBS with 1% BSA, 50% glycerol and 0.02% sodium azide; pH 7.3
• Gene Accession No.: P50897
• Gene Symbols: Ppt1
• Immunogen: Human recombinant protein fragment corresponding to amino acids 100-306 of PPT1 produced in E.coli.
• Quantity: 100 μL
• Primary or Secondary: Primary
• Target Species: Human
• Product Type: Antibody
• Isotype: IgG1

• Applications: Immunohistochemistry (Paraffin), Western Blot
• Clone: OTI1F10
• Conjugate: Unconjugated
• Gene: Ppt1
• Gene Alias: 3.1.2.22; 9530043G02Rik; AA960502; C77813; ceroid-palmitoyl-palmitoyl-protein thioesterase 1; CLN1; D4Ertd184e; INCL; Palmitoyl-protein hydrolase 1; palmitoyl-protein thioesterase; palmitoyl-protein thioesterase 1; palmitoyl-protein thioesterase 1 (ceroid-lipofuscinosis, neuronal 1, infantile); PPT; Ppt1; PPT-1; QnpA-18851; unnamed protein product
• Host Species: Mouse
• Purification Method: Affinity Chromatography
• Regulatory Status: RUO
• Gene ID (Entrez): 5538
• Content And Storage: -20°C, Avoid Freeze/Thaw Cycles
• Form: Liquid